Scleroderma Renal Crisis
Here's a nice visual for diagnosis and treatment of systemic sclerosis renal crisis. For diagnosis just think of a patient who has systemic sclerosis who has a new AKI, HTN with a normal urinalysis/urine sediment (but may have mild proteinuria), and signs of MAHA. Usually it is diagnosed within the first 4 years after diagnosis of diffuse cutaneous SSc. For treatment, Captain Captopril comes to save the day. You bring the blood pressure back to normal within 72 hours. His side-kick nitroprusside helps when there is CNS involvement of the renal crisis (eg encephalopathy, papilledema).
References:Denton, C. (2021, August 30). Overview of the treatment and prognosis of systemic sclerosis (scleroderma) in adults. UpToDate. Retrieved February 17, 2022, from https://www.uptodate.com/contents/overview-of-the-treatment-and-prognosis-of-systemic-sclerosis-scleroderma-in-adults?search=scleroderma+treatment&source=search_result&selectedTitle=1~150&usage_type=default&display_rank=1
Published:January 11, 2021